Posterior Cortical Atrophy with Acute Onset and Rapid Progressive Visual Symptoms: A Case Report

초록

Background Posterior cortical atrophy (PCA) is characterized by slowly progressive early onset dementia with cortical visual dysfunctionand disproportionate atrophy of the posterior cortex. Case Report A 55-year-old right-handed woman developed visuo-spatial impairments that progressed rapidly into cortical blindness overthe following 3 months. Neuro-psychological evaluation revealed Gerstmann syndrome and severe constructional impairments with all componentsof Balint syndrome. However, her memory, insight, and judgment were preserved. Her brain MRI was normal. However, 18F fluorodeoxyglucosepositron emission tomography revealed a marked hypometabolism in the bilateral parieto-occipital region. Conclusions Although rapid progression of visuo-spatial dysfunction without memory impairment occurred, we considered PCA as well.

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